Spontaneous cerebrospinal fluid otorrhea in association with a congenital defect of the cochlear aqueduct and Mondini dysplasia

T. S. Park, H. J. Hoffman, R. P. Humphreys, S. H. Chuang

Research output: Contribution to journalArticlepeer-review

35 Scopus citations

Abstract

Unrecognized spontaneous cerebrospinal fluid (CSF) otorrhea led to recurrent bacterial meningitis in three children. The underlying cause of the spontaneous CSF otorrhea was proved to be a congenital cystic dilatation of the cochlear aqueduct and Mondini dysplasia of the temporal bone. The CSF leak recurred in all patients after an initial surgical attempt to close the defects through a tympanotomy. A suboccipital approach was used successfully to obliterate the CSF fistulas in two children; a translabyrinthine approach was used in the other. A search of the literature revealed that Mondini dysplasia is a congenital anomaly that can commonly cause spontaneous CSF otorrhea in children. The authors discuss the management of this uncommon entity on the basis of a literature review and their own experience.

Original languageEnglish
Pages (from-to)356-362
Number of pages7
JournalNeurosurgery
Volume11
Issue number3
DOIs
StatePublished - Jan 1 1982
Externally publishedYes

Fingerprint Dive into the research topics of 'Spontaneous cerebrospinal fluid otorrhea in association with a congenital defect of the cochlear aqueduct and Mondini dysplasia'. Together they form a unique fingerprint.

Cite this