We report the first case of a child with hemophagocytic lymphohistiocytosis (HLH) who presented with signs and symptoms mimicking acute appendicitis. Laparoscopy demonstrated ulcerated small intestinal plaques, and microscopic examination of that tissue showed necroinflammatory exudate and erythrophagocytosis. HLH manifesting as small intestinal ulcers has not been previously described.
- Hemophagocytic lymphohistiocytosis
- Small intestinal ulcers