Scimitar syndrome in childhood

Charles E. Canter, Thomas C. Martin, Thomas L. Spray, Clarence S. Weldon, Arnold W. Strauss

Research output: Contribution to journalArticlepeer-review

66 Scopus citations


Scimitar syndrome is a rare but well-described constellation of cardiopulmonary anomalies: anomalous pulmonary venous connection of the right lung, hypoplasia of the right lung with dextroposition of the heart, hypoplasia and malformation of the right pulmonary artery (PA) and bronchial trees, and anomalous systemic arterial blood supply to the right lung, arising from the abdominal aorta or its branches. The partial or total anomalous venous connection of the right lung drains into the inferior vena cava or azygous system and is present in all cases.1-5 Often, this anomalous vessel is visible on a chest radiograph as a curvilinear shadow just above the right diaphragm and resembles a Turkish sword or "scimitar." This report summarizes our experience with scimitar syndrome in 15 children.

Original languageEnglish
Pages (from-to)652-654
Number of pages3
JournalThe American journal of cardiology
Issue number7
StatePublished - Sep 15 1986


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