TY - JOUR
T1 - Pulmonary venoocclusive disease
T2 - case report and review of the literature
AU - Shackelford, G. D.
AU - Sacks, E. J.
AU - Mullins, J. D.
AU - McAlister, W. H.
PY - 1977
Y1 - 1977
N2 - A fatal case of pulmonary venoocclusive disease in a 4-year-old boy is reported, with emphasis on the radiologic features of this condition. The disease is characterized by fibrous intimal obliteration of the lumina of small pulmonary veins and venules leading to severe secondary pulmonary arterial hypertension. The clinical picture is usually indistinguishable from that of other forms of pulmonary arterial hypertension, but radiologic features of postcapillary pulmonary hypertension, in conjunction with a normal pulmonary wedge pressure, are suggestive of pulmonary venoocclusive disease. The diagnosis is definitively established by lung biopsy.
AB - A fatal case of pulmonary venoocclusive disease in a 4-year-old boy is reported, with emphasis on the radiologic features of this condition. The disease is characterized by fibrous intimal obliteration of the lumina of small pulmonary veins and venules leading to severe secondary pulmonary arterial hypertension. The clinical picture is usually indistinguishable from that of other forms of pulmonary arterial hypertension, but radiologic features of postcapillary pulmonary hypertension, in conjunction with a normal pulmonary wedge pressure, are suggestive of pulmonary venoocclusive disease. The diagnosis is definitively established by lung biopsy.
UR - http://www.scopus.com/inward/record.url?scp=0017332521&partnerID=8YFLogxK
U2 - 10.2214/ajr.128.4.643
DO - 10.2214/ajr.128.4.643
M3 - Article
C2 - 403796
AN - SCOPUS:0017332521
SN - 0361-803X
VL - 128
SP - 643
EP - 648
JO - American Journal of Roentgenology
JF - American Journal of Roentgenology
IS - 4
ER -