Abstract
We report on an African-American male with Cantu syndrome who required a pericardial window for a significant pericardial effusion in infancy and was subsequently found to have partial pulmonary venous obstruction (PVO) leading to pulmonary hypertension. Measurement of bilateral pulmonary capillary wedge pressures is important to uncover partial PVO.
Original language | English |
---|---|
Pages (from-to) | 727-729 |
Number of pages | 3 |
Journal | Pediatric Pulmonology |
Volume | 45 |
Issue number | 7 |
DOIs | |
State | Published - Jul 2010 |
Keywords
- Cardiomegaly
- Genetic syndrome
- Mean pulmonary capillary wedge pressure
- Pericardial effusion
- Pericardial window