Protein Losing Enteropathy After Fontan Operation: Glimpses of Clarity Through the Lifting Fog

Jack Rychik; Kathryn M. Dodds; David Goldberg; Andrew C. Glatz; Mark Fogel; Joseph Rossano; Jonathan Chen; Erin Pinto; Chitra Ravishankar; Elizabeth Rand; Jonathan J. Rome; Yoav Dori

doi:10.1177/2150135119890555

Protein Losing Enteropathy After Fontan Operation: Glimpses of Clarity Through the Lifting Fog

Jack Rychik, Kathryn M. Dodds, David Goldberg, Andrew C. Glatz, Mark Fogel, Joseph Rossano, Jonathan Chen, Erin Pinto, Chitra Ravishankar, Elizabeth Rand, Jonathan J. Rome, Yoav Dori

Research output: Contribution to journal › Article › peer-review

28 Scopus citations

Abstract

Fontan-associated protein losing enteropathy is a challenge to treat and is a major contributor to morbidity and mortality in patients with palliated single ventricle. Numerous strategies for management have been proposed, with confusion as to how best to stratify and implement care among the many treatments available. Medical management can be helpful in some, while novel lymphatic interventions hold potential for remission with good results. We review our institutional approach to protein losing enteropathy after Fontan operation and provide a suggested algorithm and pathway for effective care.

Original language	English
Pages (from-to)	92-96
Number of pages	5
Journal	World Journal for Pediatric and Congenital Heart Surgery
Volume	11
Issue number	1
DOIs	https://doi.org/10.1177/2150135119890555
State	Published - Jan 1 2020

Keywords

Fontan
lymphatics
protein losing enteropathy
single ventricle

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10.1177/2150135119890555

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abstract = "Fontan-associated protein losing enteropathy is a challenge to treat and is a major contributor to morbidity and mortality in patients with palliated single ventricle. Numerous strategies for management have been proposed, with confusion as to how best to stratify and implement care among the many treatments available. Medical management can be helpful in some, while novel lymphatic interventions hold potential for remission with good results. We review our institutional approach to protein losing enteropathy after Fontan operation and provide a suggested algorithm and pathway for effective care.",

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AU - Dodds, Kathryn M.

AU - Goldberg, David

AU - Glatz, Andrew C.

AU - Fogel, Mark

AU - Rossano, Joseph

AU - Chen, Jonathan

AU - Pinto, Erin

AU - Ravishankar, Chitra

AU - Rand, Elizabeth

AU - Rome, Jonathan J.

AU - Dori, Yoav

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Y1 - 2020/1/1

N2 - Fontan-associated protein losing enteropathy is a challenge to treat and is a major contributor to morbidity and mortality in patients with palliated single ventricle. Numerous strategies for management have been proposed, with confusion as to how best to stratify and implement care among the many treatments available. Medical management can be helpful in some, while novel lymphatic interventions hold potential for remission with good results. We review our institutional approach to protein losing enteropathy after Fontan operation and provide a suggested algorithm and pathway for effective care.

AB - Fontan-associated protein losing enteropathy is a challenge to treat and is a major contributor to morbidity and mortality in patients with palliated single ventricle. Numerous strategies for management have been proposed, with confusion as to how best to stratify and implement care among the many treatments available. Medical management can be helpful in some, while novel lymphatic interventions hold potential for remission with good results. We review our institutional approach to protein losing enteropathy after Fontan operation and provide a suggested algorithm and pathway for effective care.

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Protein Losing Enteropathy After Fontan Operation: Glimpses of Clarity Through the Lifting Fog

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