Pancreas

Disorders of the pancreas can origin from congenital structural abnormalities such as annular pancreas, pancreas divisum and pancreaticobiliary malunion and may require surgical interventions. Congenital hyperinsulinism (CHI) is a rare and complex genetic disorder, that can present with a focal, diffuse or atypical lesion. Near-total pancreatectomy is the procedure of choice for diffuse CHI, whereas a localized resection is curative for focal CHI. An increasing incidence of pancreatitis in children has been reported recently-likely due to the increased incidence of obesity, drug associated pancreatitis and improvements in detection. Benign and malignant pancreatic tumors are relatively uncommon in children, thus making diagnosis, classification and management challenging.