Nummular keratopathy in a patient with Hyper-IgD Syndrome

Courtney L. Kraus, Susan M. Culican

Research output: Contribution to journalArticlepeer-review

14 Scopus citations


Purpose: To report a case of recurrent nummular keratitis in a pediatric patient with Hyperimmunoglobulinemia D syndrome. Methods: A retrospective chart review. Results: A 14-year-old boy with Hyperimmunoglobulinemia D syndrome (HIDS) presented with photophobia and ocular irritation concomitant with disease exacerbation. He was found on exam to have significant nummular keratitis, which responded to a short course of topical steroids. Despite acute response to local immunosuppression, the patient had several recurrent attacks and eventually developed a large corneal scar and decreased vision. After initiation of infliximab therapy his ocular sequelae improved dramatically and his vision returned to 20/20. Conclusion: One possible form of end-organ damage associated with HIDS is vision threatening nummular keratopathy.

Original languageEnglish
Article number14
JournalPediatric Rheumatology
StatePublished - Aug 5 2009


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