Non-Peutz-Jeghers syndrome-associated ovarian sex cord tumor with annular tubules: Report of a malignant case

Ying Han, Shumin Li, Lingying Wu, Xun Zhang, Dengfeng Cao

Research output: Contribution to journalArticlepeer-review

8 Scopus citations

Abstract

A sex cord tumor with annular tubules (SCTAT) is a rare but distinctive subtype of sex cord stromal tumor of the ovary. Its clinical features depend on an association with Peutz-Jeghers syndrome (PJS). SCTAT associated with PJS typically manifests as bilateral, multifocal, and small lesions and is clinically benign. In contrast, SCTAT not associated with PJS often manifests as a unilateral large mass and 20% of such tumors have malignant potential. Most patients with SCTAT are diagnosed at stage I, and metastasis is rare. Here we present a case of malignant SCTAT of stage III A1(ii) (retroperitoneal lymph node metastasis, largest dimension of metastasis >10 mm) in a 14-year-old girl without PJS.

Original languageEnglish
Pages (from-to)224-227
Number of pages4
JournalJournal of Obstetrics and Gynaecology Research
Volume42
Issue number2
DOIs
StatePublished - Feb 1 2016

Keywords

  • Peutz-Jeghers syndrome
  • behavior
  • metastasis
  • sex cord tumor with annular tubules

Fingerprint

Dive into the research topics of 'Non-Peutz-Jeghers syndrome-associated ovarian sex cord tumor with annular tubules: Report of a malignant case'. Together they form a unique fingerprint.

Cite this