Moyamoya syndrome associated with hemoglobin southampton (casper)

Nader Delavari, Jennifer Strahle, Cormac O. Maher

Research output: Contribution to journalArticle

5 Scopus citations

Abstract

When moyamoya vasculopathy results from an associated disease, this vasculopathy is then referred to as moyamoya syndrome. Moyamoya syndrome has been reported in association with sickle cell disease, neurofibromatosis type 1, Down syndrome, radiation exposure, and other predisposing factors. Other than sickle cell disease, rare hemoglobinopathies, such as hemoglobin Fairfax and hemoglobin Alesha, have been reported to occur with moyamoya. We present a case of moyamoya syndrome associated with an unstable hemoglobinopathy, hemoglobin Southampton (Casper). This is the first reported case of moyamoya associated with this hemoglobinopathy.

Original languageEnglish
Pages (from-to)307-310
Number of pages4
JournalPediatric Neurosurgery
Volume49
Issue number5
DOIs
StatePublished - Nov 27 2013
Externally publishedYes

Keywords

  • Hemoglobinopathy
  • Moyamoya
  • Pial synangiosis

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