Massive global right ventricular hypertrophy with both fixed and dynamic obstruction and pulmonary valve dysplasia

Ari M. Cedars, Cylen Javidan-Nejad, Manu Goyal, Joseph Billadello, Philip Ludbrook

Research output: Contribution to journalArticle

Abstract

Congenital pulmonary valvular dysplasia is an unusual condition typically associated with Noonan syndrome. Among its other cardiac manifestations, occasional patients with Noonan syndrome have been demonstrated to have hypertrophic nonobstructive cardiomyopathy, which may be biventricular. We report a unique case of pulmonary valvular dysplasia, dynamic right ventricular outflow tract obstruction and profound right ventricular hypertrophy with only mild left ventricular hypertrophy, in a patient without Noonan syndrome.

Original languageEnglish
Pages (from-to)66-70
Number of pages5
JournalCongenital Heart Disease
Volume7
Issue number1
DOIs
StatePublished - Jan 1 2012

Keywords

  • Dynamic right ventricular outflow tract obstruction
  • Hypertrophic cardiomyopathy
  • Noonan syndrome
  • Pulmonary valve dysplasia
  • Right ventricular hypertrophy

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