TY - JOUR
T1 - Hemangioendothelioma
T2 - A rare case of a primary intracardiac tumor
AU - Beaton, Andrea
AU - Kuttler, Trevor
AU - Hassan, Ali
AU - Nath, Dilip S.
AU - Reyes, Christine
AU - Jonas, Richard A.
AU - Martin, Gerard R.
PY - 2013/1/1
Y1 - 2013/1/1
N2 - Kaposiform hemangioendothelioma (KH) is a rare tumor of vascular origin that commonly affects the cutaneous tissues of the extremities. It can, however, affect the abdomen, thorax, head, or neck. Compared with juvenile hemangiomas, which tend to regress, KH tumors are locally aggressive and usually persist. Associated morbidity and mortality rates range from 12 to 30 % and typically are related to either compressive effects on surrounding vital structures or effects of the Kasabach-Merritt phenomenon [10, 11, 13]. To our knowledge, this report is the first to describe KH presenting as a primary intracardiac tumor.
AB - Kaposiform hemangioendothelioma (KH) is a rare tumor of vascular origin that commonly affects the cutaneous tissues of the extremities. It can, however, affect the abdomen, thorax, head, or neck. Compared with juvenile hemangiomas, which tend to regress, KH tumors are locally aggressive and usually persist. Associated morbidity and mortality rates range from 12 to 30 % and typically are related to either compressive effects on surrounding vital structures or effects of the Kasabach-Merritt phenomenon [10, 11, 13]. To our knowledge, this report is the first to describe KH presenting as a primary intracardiac tumor.
KW - Cardiac tumor
KW - Pediatric cardiology
KW - Pericardial effusion
UR - https://www.scopus.com/pages/publications/84872601822
U2 - 10.1007/s00246-012-0280-1
DO - 10.1007/s00246-012-0280-1
M3 - Article
C2 - 22421960
AN - SCOPUS:84872601822
SN - 0172-0643
VL - 34
SP - 194
EP - 197
JO - Pediatric Cardiology
JF - Pediatric Cardiology
IS - 1
ER -