TY - JOUR
T1 - Harlequin Ichthyosis
T2 - A Surgical Perspective
AU - Pet, Mitchell A.
AU - Gupta, Deepti
AU - Tse, Raymond W.
N1 - Publisher Copyright:
© 2016 Wiley Periodicals, Inc.
PY - 2016/9/1
Y1 - 2016/9/1
N2 - Limb constriction or encasement in patients with harlequin ichthyosis can cause tissue injury resulting in necrosis and auto-amputation. Surgical release of constrictive plaques has been previously demonstrated, but the perioperative and intraoperative considerations surrounding this infrequent intervention have not been discussed in detail. This report documents a case of harlequin ichthyosis requiring surgical treatment, focusing on the importance of early surgical consultation, risks of surgery, indications for and timing of surgical intervention, and the details of the operation.
AB - Limb constriction or encasement in patients with harlequin ichthyosis can cause tissue injury resulting in necrosis and auto-amputation. Surgical release of constrictive plaques has been previously demonstrated, but the perioperative and intraoperative considerations surrounding this infrequent intervention have not been discussed in detail. This report documents a case of harlequin ichthyosis requiring surgical treatment, focusing on the importance of early surgical consultation, risks of surgery, indications for and timing of surgical intervention, and the details of the operation.
UR - http://www.scopus.com/inward/record.url?scp=84985995470&partnerID=8YFLogxK
U2 - 10.1111/pde.12944
DO - 10.1111/pde.12944
M3 - Article
C2 - 27470191
AN - SCOPUS:84985995470
SN - 0736-8046
VL - 33
SP - e327-e332
JO - Pediatric Dermatology
JF - Pediatric Dermatology
IS - 5
ER -