TY - JOUR
T1 - Grisel's syndrome
T2 - A rare cause of torticollis with subluxation of the atlantoaxial joint secondary to a retropharyngeal abscess
AU - White, Michael D.
AU - Hansberry, David R.
AU - Prabhu, Arpan V.
AU - Agarwal, Nitin
AU - Kandula, Vinay
N1 - Publisher Copyright:
© 2020 The Authors
PY - 2020/12
Y1 - 2020/12
N2 - Background: Atraumatic rotary subluxation of the atlantoaxial joint (Grisel's syndrome) is a rare cause of torticollis. Although rare, prompt recognition and treatment of this disorder is essential in preventing permanent deformity. Case presentation A 4-year-old female with no significant past medical history presented to the emergency department (ED) after an outpatient positive streptococcus test with intermittent subjective fevers for one week. In the ED, the patient had a temperature of 103.0 F and was found to have a leukocytosis of 26,700 K/UL with a leftward shift of neutrophils. Initial radiograph of the neck found asymmetric soft tissue fullness and increased opacity in the right upper and mid cervical neck. Subsequently, contrast-enhanced computed tomography (CT) of the soft tissues of the neck found a right-sided retropharyngeal abscess measuring 1.5 cm. It was located medial to the carotid space with surrounding edema, inflammation, and fluid tracking inferiorly along the prevertebral soft tissues. There was associated lateral displacement of the right cervical internal carotid artery and jugular veins with regional stenosis. Additionally, there was atlantoaxial subluxation of C1 on C2. The patient was medically managed with intravenous antibiotics. The patient received dexamethasone for the edema and was admitted as an inpatient. She subsequently improved and had an uneventful hospital course with discharge to home. Conclusions: Grisel's syndrome is an infrequent diagnosis, which is seen with atlantoaxial rotary subluxation accompanying infection or recent otolaryngolic surgery. Diagnosis typically requires cross-sectional imaging, often with CT. Without treatment with reduction and immobilization, there can be permanent fixed deformity.
AB - Background: Atraumatic rotary subluxation of the atlantoaxial joint (Grisel's syndrome) is a rare cause of torticollis. Although rare, prompt recognition and treatment of this disorder is essential in preventing permanent deformity. Case presentation A 4-year-old female with no significant past medical history presented to the emergency department (ED) after an outpatient positive streptococcus test with intermittent subjective fevers for one week. In the ED, the patient had a temperature of 103.0 F and was found to have a leukocytosis of 26,700 K/UL with a leftward shift of neutrophils. Initial radiograph of the neck found asymmetric soft tissue fullness and increased opacity in the right upper and mid cervical neck. Subsequently, contrast-enhanced computed tomography (CT) of the soft tissues of the neck found a right-sided retropharyngeal abscess measuring 1.5 cm. It was located medial to the carotid space with surrounding edema, inflammation, and fluid tracking inferiorly along the prevertebral soft tissues. There was associated lateral displacement of the right cervical internal carotid artery and jugular veins with regional stenosis. Additionally, there was atlantoaxial subluxation of C1 on C2. The patient was medically managed with intravenous antibiotics. The patient received dexamethasone for the edema and was admitted as an inpatient. She subsequently improved and had an uneventful hospital course with discharge to home. Conclusions: Grisel's syndrome is an infrequent diagnosis, which is seen with atlantoaxial rotary subluxation accompanying infection or recent otolaryngolic surgery. Diagnosis typically requires cross-sectional imaging, often with CT. Without treatment with reduction and immobilization, there can be permanent fixed deformity.
KW - Grisel syndrome
KW - Grisel's syndrome
KW - Retropharyngeal abscess
KW - Subluxation
KW - Torticollis
UR - http://www.scopus.com/inward/record.url?scp=85089824845&partnerID=8YFLogxK
U2 - 10.1016/j.inat.2020.100872
DO - 10.1016/j.inat.2020.100872
M3 - Article
AN - SCOPUS:85089824845
SN - 2214-7519
VL - 22
JO - Interdisciplinary Neurosurgery: Advanced Techniques and Case Management
JF - Interdisciplinary Neurosurgery: Advanced Techniques and Case Management
M1 - 100872
ER -