Fibrous dysplasia with cartilaginous differentiation ("fibrocartilaginous dysplasia"): A review, with an illustrative case followed for 18 years

Michael Kyriakos, Douglas J. McDonald, Murali Sundaram

Research output: Contribution to journalReview articlepeer-review

34 Scopus citations

Abstract

A 21-year-old man with an 18-year history of progressive, and deforming, monomelic fibrous dysplasia with massive cartilaginous differentiation (fibrocartilaginous dysplasia) is described. A review is made of all prior reported examples of this entity in the English language medical literature. The radiologic and histologic differential diagnoses are described, distinguishing the lesion from chondrosarcoma and from fibrocartilaginous mesenchymoma.

Original languageEnglish
Pages (from-to)51-62
Number of pages12
JournalSkeletal Radiology
Volume33
Issue number1
DOIs
StatePublished - Jan 2004

Keywords

  • Fibrocartilaginous dysplasia
  • Fibrocartilaginous mesenchymoma
  • Fibrous dysplasia

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