Febrile ulceronecrotic mucha-habermann disease with central nervous system vasculitis

Ilana S. Rosman, Ling Chih Liang, Sushama Patil, Susan J. Bayliss, Andrew J. White

Research output: Contribution to journalArticlepeer-review

10 Scopus citations


Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a severe variant of pityriasis lichenoides et varioliformis acuta (PLEVA). We report a case of FUMHD in an 11-year-old boy who subsequently developed neurologic symptoms and was found to have necrotizing vasculitis on brain biopsy. Over 5 years of follow-up, he had one biopsy-proven recurrence of his skin lesions and continued rehabilitation and treatment for residual neurologic complications. This case provides histological evidence of central nervous system vasculitis associated with FUMHD. Our patient's disease was eventually controlled with cyclophosphamide.

Original languageEnglish
Pages (from-to)90-93
Number of pages4
JournalPediatric Dermatology
Issue number1
StatePublished - Jan 1 2013

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