Double lung transplantation for end-stage Kartagener syndrome: A case report and literature review

Bo Wang; Xinghua Zhang; Wenyang Jiang; Jie Huang; Jingyu Chen; Daniel Kreisel; Jose Luis J. Danguilan; Michael Hsin; Huiqing Lin

doi:10.21037/jtd.2020.02.28

Double lung transplantation for end-stage Kartagener syndrome: A case report and literature review

Bo Wang, Xinghua Zhang, Wenyang Jiang, Jie Huang, Jingyu Chen, Daniel Kreisel, Jose Luis J. Danguilan, Michael Hsin, Huiqing Lin

Research output: Contribution to journal › Review article

1 Scopus citations

Abstract

Kartagener syndrome (KS) is an autosomal recessive disorder characterized by situs inversus, paranasal sinusitis and bronchiectasis. We report the successful use of double lung transplant (DLTx) to treat end-stage KS. A 49-year-old Han woman was admitted to Renmin Hospital (Wuhan University, China) in September 2017 with a ≥15 year history of chronic productive cough that had worsened during the past year. Clinical examination and imaging investigations revealed respiratory failure and situs inversus consistent with KS. The patient was successfully treated with DLTx involving bilateral bronchial anastomoses. DLTx is a feasible treatment option for end-stage KS.

Original language	English
Pages (from-to)	1588-1594
Number of pages	7
Journal	Journal of Thoracic Disease
Volume	12
Issue number	4
DOIs	https://doi.org/10.21037/jtd.2020.02.28
State	Published - Apr 1 2020
Externally published	Yes

Keywords

Kartagener syndrome
Lung transplantation
Primary ciliary dyskinesia
Situs inversus

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10.21037/jtd.2020.02.28

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Wang, B., Zhang, X., Jiang, W., Huang, J., Chen, J., Kreisel, D., Danguilan, J. L. J., Hsin, M., & Lin, H. (2020). Double lung transplantation for end-stage Kartagener syndrome: A case report and literature review. Journal of Thoracic Disease, 12(4), 1588-1594. https://doi.org/10.21037/jtd.2020.02.28

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abstract = "Kartagener syndrome (KS) is an autosomal recessive disorder characterized by situs inversus, paranasal sinusitis and bronchiectasis. We report the successful use of double lung transplant (DLTx) to treat end-stage KS. A 49-year-old Han woman was admitted to Renmin Hospital (Wuhan University, China) in September 2017 with a ≥15 year history of chronic productive cough that had worsened during the past year. Clinical examination and imaging investigations revealed respiratory failure and situs inversus consistent with KS. The patient was successfully treated with DLTx involving bilateral bronchial anastomoses. DLTx is a feasible treatment option for end-stage KS.",

keywords = "Kartagener syndrome, Lung transplantation, Primary ciliary dyskinesia, Situs inversus",

author = "Bo Wang and Xinghua Zhang and Wenyang Jiang and Jie Huang and Jingyu Chen and Daniel Kreisel and Danguilan, {Jose Luis J.} and Michael Hsin and Huiqing Lin",

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Double lung transplantation for end-stage Kartagener syndrome : A case report and literature review. / Wang, Bo; Zhang, Xinghua; Jiang, Wenyang; Huang, Jie; Chen, Jingyu; Kreisel, Daniel; Danguilan, Jose Luis J.; Hsin, Michael; Lin, Huiqing.

In: Journal of Thoracic Disease, Vol. 12, No. 4, 01.04.2020, p. 1588-1594.

Research output: Contribution to journal › Review article

TY - JOUR

T1 - Double lung transplantation for end-stage Kartagener syndrome

T2 - A case report and literature review

AU - Wang, Bo

AU - Zhang, Xinghua

AU - Jiang, Wenyang

AU - Huang, Jie

AU - Chen, Jingyu

AU - Kreisel, Daniel

AU - Danguilan, Jose Luis J.

AU - Hsin, Michael

AU - Lin, Huiqing

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AB - Kartagener syndrome (KS) is an autosomal recessive disorder characterized by situs inversus, paranasal sinusitis and bronchiectasis. We report the successful use of double lung transplant (DLTx) to treat end-stage KS. A 49-year-old Han woman was admitted to Renmin Hospital (Wuhan University, China) in September 2017 with a ≥15 year history of chronic productive cough that had worsened during the past year. Clinical examination and imaging investigations revealed respiratory failure and situs inversus consistent with KS. The patient was successfully treated with DLTx involving bilateral bronchial anastomoses. DLTx is a feasible treatment option for end-stage KS.

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KW - Lung transplantation

KW - Primary ciliary dyskinesia

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