@article{f3257ed988044792ad8f0380a7252248,
title = "Diagnosis, monitoring, and treatment of primary ciliary dyskinesia: PCD foundation consensus recommendations based on state of the art review",
abstract = "Summary Primary ciliary dyskinesia (PCD) is a genetically heterogeneous, rare lung disease resulting in chronic oto-sino-pulmonary disease in both children and adults. Many physicians incorrectly diagnose PCD or eliminate PCD from their differential diagnosis due to inexperience with diagnostic testing methods. Thus far, all therapies used for PCD are unproven through large clinical trials. This review article outlines consensus recommendations from PCD physicians in North America who have been engaged in a PCD centered research consortium for the last 10 years. These recommendations have been adopted by the governing board of the PCD Foundation to provide guidance for PCD clinical centers for diagnostic testing, monitoring, and appropriate short and long-term therapeutics in PCD patients.",
keywords = "PCD Foundation, PCD, kartagener, consensus statement, primary ciliary dyskinesia",
author = "Shapiro, {Adam J.} and Zariwala, {Maimoona A.} and Thomas Ferkol and Davis, {Stephanie D.} and Sagel, {Scott D.} and Dell, {Sharon D.} and Margaret Rosenfeld and Olivier, {Kenneth N.} and Carlos Milla and Daniel, {Sam J.} and Kimple, {Adam J.} and Michele Manion and Knowles, {Michael R.} and Leigh, {Margaret W.}",
note = "Funding Information: We thank the APRN paediatricians who completed the 2013 multi-topic survey and the parent needs survey. The multi-topic survey was funded by the 2013 Royal Australasian College Physicians Fellows Award. The parent needs study was funded by the Scobie and Claire Mackinnon Trust and Southern Health. Murdoch Children''s Research Institute research is supported by the Victorian Government''s Operational Infrastructure Support Program. Publisher Copyright: {\textcopyright} 2015 Wiley Periodicals, Inc.",
year = "2016",
month = feb,
day = "1",
doi = "10.1002/ppul.23304",
language = "English",
volume = "51",
pages = "115--132",
journal = "Pediatric Pulmonology",
issn = "8755-6863",
number = "2",
}