Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome

T. E. Herman; W. H. McAlister

doi:10.1007/BF02015451

Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome

Section of Pediatric Radiology

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Abstract

Type IV Ehlers-Danlos syndrome (EDS) is characterized by large vessel bleeding, visceral rupture and early death. Pulmonary complications are uncommon. We report an 18-year-old patient with EDS type IV who developed recurrent large, thick-walled lung cavitary lesions, probably a manifestation of focal lung rupture. Such hemorrhagic cavities are probably the basis of the bullous disase and recurrent pneumothoraces occasionally observed in type IV EDS.

Original language	English
Pages (from-to)	263-265
Number of pages	3
Journal	Pediatric radiology
Volume	24
Issue number	4
DOIs	https://doi.org/10.1007/BF02015451
State	Published - Aug 1 1994

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title = "Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome",

abstract = "Type IV Ehlers-Danlos syndrome (EDS) is characterized by large vessel bleeding, visceral rupture and early death. Pulmonary complications are uncommon. We report an 18-year-old patient with EDS type IV who developed recurrent large, thick-walled lung cavitary lesions, probably a manifestation of focal lung rupture. Such hemorrhagic cavities are probably the basis of the bullous disase and recurrent pneumothoraces occasionally observed in type IV EDS.",

author = "Herman, \{T. E.\} and McAlister, \{W. H.\}",

year = "1994",

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doi = "10.1007/BF02015451",

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T1 - Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome

AU - Herman, T. E.

AU - McAlister, W. H.

PY - 1994/8/1

Y1 - 1994/8/1

N2 - Type IV Ehlers-Danlos syndrome (EDS) is characterized by large vessel bleeding, visceral rupture and early death. Pulmonary complications are uncommon. We report an 18-year-old patient with EDS type IV who developed recurrent large, thick-walled lung cavitary lesions, probably a manifestation of focal lung rupture. Such hemorrhagic cavities are probably the basis of the bullous disase and recurrent pneumothoraces occasionally observed in type IV EDS.

AB - Type IV Ehlers-Danlos syndrome (EDS) is characterized by large vessel bleeding, visceral rupture and early death. Pulmonary complications are uncommon. We report an 18-year-old patient with EDS type IV who developed recurrent large, thick-walled lung cavitary lesions, probably a manifestation of focal lung rupture. Such hemorrhagic cavities are probably the basis of the bullous disase and recurrent pneumothoraces occasionally observed in type IV EDS.

UR - https://www.scopus.com/pages/publications/0027934259

U2 - 10.1007/BF02015451

DO - 10.1007/BF02015451

M3 - Article

C2 - 7800447

AN - SCOPUS:0027934259

SN - 0301-0449

VL - 24

SP - 263

EP - 265

JO - Pediatric radiology

JF - Pediatric radiology

IS - 4

ER -

Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome

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