Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome

T. E. Herman; W. H. McAlister

doi:10.1007/BF02015451

Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome

T. E. Herman, W. H. McAlister

Section of Pediatric Radiology

Research output: Contribution to journal › Article › peer-review

27 Scopus citations

Abstract

Type IV Ehlers-Danlos syndrome (EDS) is characterized by large vessel bleeding, visceral rupture and early death. Pulmonary complications are uncommon. We report an 18-year-old patient with EDS type IV who developed recurrent large, thick-walled lung cavitary lesions, probably a manifestation of focal lung rupture. Such hemorrhagic cavities are probably the basis of the bullous disase and recurrent pneumothoraces occasionally observed in type IV EDS.

Original language	English
Pages (from-to)	263-265
Number of pages	3
Journal	Pediatric radiology
Volume	24
Issue number	4
DOIs	https://doi.org/10.1007/BF02015451
State	Published - Aug 1 1994

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title = "Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome",

abstract = "Type IV Ehlers-Danlos syndrome (EDS) is characterized by large vessel bleeding, visceral rupture and early death. Pulmonary complications are uncommon. We report an 18-year-old patient with EDS type IV who developed recurrent large, thick-walled lung cavitary lesions, probably a manifestation of focal lung rupture. Such hemorrhagic cavities are probably the basis of the bullous disase and recurrent pneumothoraces occasionally observed in type IV EDS.",

author = "Herman, {T. E.} and McAlister, {W. H.}",

year = "1994",

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AU - Herman, T. E.

AU - McAlister, W. H.

PY - 1994/8/1

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N2 - Type IV Ehlers-Danlos syndrome (EDS) is characterized by large vessel bleeding, visceral rupture and early death. Pulmonary complications are uncommon. We report an 18-year-old patient with EDS type IV who developed recurrent large, thick-walled lung cavitary lesions, probably a manifestation of focal lung rupture. Such hemorrhagic cavities are probably the basis of the bullous disase and recurrent pneumothoraces occasionally observed in type IV EDS.

AB - Type IV Ehlers-Danlos syndrome (EDS) is characterized by large vessel bleeding, visceral rupture and early death. Pulmonary complications are uncommon. We report an 18-year-old patient with EDS type IV who developed recurrent large, thick-walled lung cavitary lesions, probably a manifestation of focal lung rupture. Such hemorrhagic cavities are probably the basis of the bullous disase and recurrent pneumothoraces occasionally observed in type IV EDS.

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U2 - 10.1007/BF02015451

DO - 10.1007/BF02015451

M3 - Article

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AN - SCOPUS:0027934259

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VL - 24

SP - 263

EP - 265

JO - Pediatric radiology

JF - Pediatric radiology

IS - 4

ER -

Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome

Abstract

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