Auditory neuropathy (AN) is characterized by clinical hearing impairment in which the auditory brainstem response is absent or severely abnormal in the presence of normal outer cell function as measured by evoked otoacoustic emissions and cochlear microphonic. Behavioral audiometric thresholds vary and cannot be predicted based on electrophysiologic testing. Amplification and cochlear implantation in children with AN has been reported to have mixed results. The purpose of this study is to examine our experience in the rehabilitation of pediatric patients with AN.
- Auditory neuropathy/Dys-synchrony
- Cochlear implantation
- Hearing loss
- Hearing rehabilitation