Approach to a child with hemophilia B and anaphylaxis to factor IX

Surbhi Saini; Amy L. Dunn

doi:10.1007/978-3-030-31661-7_4

Approach to a child with hemophilia B and anaphylaxis to factor IX

Research output: Chapter in Book/Report/Conference proceeding › Chapter › peer-review

Abstract

The development of inhibitory antibodies is the most challenging complication in the management of patients with hemophilia. Although much rarer than the occurrence of inhibitors in hemophilia A, the development of inhibitors in patients with hemophilia B can be complicated by anaphylactoid reactions. Immune tolerance therapy in patients with hemophilia B has a lower success rate than in patients with hemophilia B and can lead to the development of steroid-resistant nephrotic syndrome.

Original language	English
Title of host publication	Pediatric Bleeding Disorders
Subtitle of host publication	A Clinical Casebook
Publisher	Springer International Publishing
Pages	35-48
Number of pages	14
ISBN (Electronic)	9783030316617
ISBN (Print)	9783030316600
DOIs	https://doi.org/10.1007/978-3-030-31661-7_4
State	Published - Jan 1 2020

Keywords

Anaphylaxis
Hemophilia B
Inhibitors

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10.1007/978-3-030-31661-7_4

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Approach to a child with hemophilia B and anaphylaxis to factor IX

Abstract

Keywords

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