TY - JOUR
T1 - Anomalous Origin of Left Pulmonary Artery From the Aorta
T2 - A Rare Entity in Congenital Heart Disease
AU - Gropler, Melanie R.F.
AU - Dalal, Aarti S.
AU - Bierhals, Andrew J.
AU - Romberg, Erin
AU - Singh, Gautam K.
AU - Manning, Peter B.
N1 - Publisher Copyright:
© 2019 The Society of Thoracic Surgeons
PY - 2019/3
Y1 - 2019/3
N2 - Anomalous origin of the left pulmonary artery (ALPA) from the aorta is a rare form of congenital heart disease, leading to long-term morbidity if not treated early. There is a reported association of this anomaly with 22q11 microdeletion syndrome. Surgical repair is commonly performed by direct reimplantation to the main pulmonary artery with or without patch or flap techniques. This report presents two unique cases of ALPA, describing embryologic considerations for morphogenesis of ALPA with 22q11 microdeletion syndrome and a novel surgical technique involving unroofing of the unique anatomy of the common wall between the left and main pulmonary arteries.
AB - Anomalous origin of the left pulmonary artery (ALPA) from the aorta is a rare form of congenital heart disease, leading to long-term morbidity if not treated early. There is a reported association of this anomaly with 22q11 microdeletion syndrome. Surgical repair is commonly performed by direct reimplantation to the main pulmonary artery with or without patch or flap techniques. This report presents two unique cases of ALPA, describing embryologic considerations for morphogenesis of ALPA with 22q11 microdeletion syndrome and a novel surgical technique involving unroofing of the unique anatomy of the common wall between the left and main pulmonary arteries.
UR - http://www.scopus.com/inward/record.url?scp=85061640511&partnerID=8YFLogxK
U2 - 10.1016/j.athoracsur.2018.07.083
DO - 10.1016/j.athoracsur.2018.07.083
M3 - Article
C2 - 30278169
AN - SCOPUS:85061640511
SN - 0003-4975
VL - 107
SP - e181-e182
JO - Annals of Thoracic Surgery
JF - Annals of Thoracic Surgery
IS - 3
ER -