Anesthesia for a 16-month-old patient with Prader-Willi syndrome

Basak C. Meco; Zekeriyya Alanoglu; Ozgur Sinan Cengiz; Neslihan Alkis

doi:10.1007/s00540-010-1005-3

Anesthesia for a 16-month-old patient with Prader-Willi syndrome

Basak C. Meco, Zekeriyya Alanoglu, Ozgur Sinan Cengiz, Neslihan Alkis

Division of General Anesthesia

Research output: Contribution to journal › Article › peer-review

5 Scopus citations

Abstract

Prader-Willi syndrome (PWS) is a rare disorder of chromosome abnormalities in which the paternal genes in chromosome 15 are lacking. The clinical course is characterized by hypotonia, hyperphagia, and morbid obesity. Both general and regional anesthesia in these patients is difficult due to morbid obesity and hypotonia. We report our anesthetic management in a patient with PWS with a body mass index (BMI) of 29.43 kg/m² who underwent orchiopexy and hypospadias repair. The clinical course of the patient was uneventful during the procedure and postoperative period. However, arrangements with a pediatric intensive care setting for the postoperative period are recommended for patients with PWS undergoing surgery.

Original language	English
Pages (from-to)	949-950
Number of pages	2
Journal	Journal of Anesthesia
Volume	24
Issue number	6
DOIs	https://doi.org/10.1007/s00540-010-1005-3
State	Published - Dec 1 2010

Keywords

Anesthesia
Hypotonia
Prader-Willi syndrome

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abstract = "Prader-Willi syndrome (PWS) is a rare disorder of chromosome abnormalities in which the paternal genes in chromosome 15 are lacking. The clinical course is characterized by hypotonia, hyperphagia, and morbid obesity. Both general and regional anesthesia in these patients is difficult due to morbid obesity and hypotonia. We report our anesthetic management in a patient with PWS with a body mass index (BMI) of 29.43 kg/m2 who underwent orchiopexy and hypospadias repair. The clinical course of the patient was uneventful during the procedure and postoperative period. However, arrangements with a pediatric intensive care setting for the postoperative period are recommended for patients with PWS undergoing surgery.",

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AU - Alkis, Neslihan

PY - 2010/12/1

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AB - Prader-Willi syndrome (PWS) is a rare disorder of chromosome abnormalities in which the paternal genes in chromosome 15 are lacking. The clinical course is characterized by hypotonia, hyperphagia, and morbid obesity. Both general and regional anesthesia in these patients is difficult due to morbid obesity and hypotonia. We report our anesthetic management in a patient with PWS with a body mass index (BMI) of 29.43 kg/m2 who underwent orchiopexy and hypospadias repair. The clinical course of the patient was uneventful during the procedure and postoperative period. However, arrangements with a pediatric intensive care setting for the postoperative period are recommended for patients with PWS undergoing surgery.

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Anesthesia for a 16-month-old patient with Prader-Willi syndrome

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