An unusual pathologic feature associated with dermatomyositis

Jacinda B. Sampson, Steven S. Chin, Frederic C. Clayton, Alan Pestronk, Kathryn J. Swoboda, Kevin M. Flanigan

Research output: Contribution to journalArticlepeer-review

1 Scopus citations


We present a case of juvenile dermatomyositis with unusual histopathologic findings. The child presented with a course consistent with dermatomyositis, a diagnosis confirmed by finding reticulotubular aggregates in endothelial cells on electron microscopy. However, histopathology of his muscle biopsy revealed a striking pattern of glycogen accumulation, to an extent similar to that seen in glycogen storage diseases; this degree of accumulation could potentially confound histopathologic diagnosis.

Original languageEnglish
Pages (from-to)391-393
Number of pages3
JournalNeuromuscular Disorders
Issue number6
StatePublished - Jun 1 2006


  • Anasarca
  • Glycogen
  • Myositis
  • Pediatric dermatomyositis
  • Reticulotubular aggregates


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