TY - JOUR
T1 - A Rare Case of Pulmonary Artery Sling and Complete Atrioventricular Canal Defect in an Infant With Trisomy 21
AU - Alsaied, Tarek
AU - Sticka, Joshua
AU - Unaka, Ndidi
AU - Cooper, David S.
AU - Manning, Peter B.
PY - 2014/7
Y1 - 2014/7
N2 - Pulmonary artery sling is a very rare congenital vascular anomaly. Patients usually present in infancy with symptoms of airway compression. Patients with trisomy 21 often have upper airway obstruction, most commonly related to pharyngeal causes or subglottic stenosis. Although the incidence of congenital heart defects in patients with trisomy 21 is very high, a review of the literature showed only one previously reported case of pulmonary artery sling in an infant with trisomy 21. We report a case of pulmonary artery sling and complete atrioventricular canal defect in a one-month-old female with trisomy 21. Echocardiography is an important diagnostic method for pulmonary artery sling, but this anomaly may be easily overlooked in the presence of more commonly anticipated defects in this population.
AB - Pulmonary artery sling is a very rare congenital vascular anomaly. Patients usually present in infancy with symptoms of airway compression. Patients with trisomy 21 often have upper airway obstruction, most commonly related to pharyngeal causes or subglottic stenosis. Although the incidence of congenital heart defects in patients with trisomy 21 is very high, a review of the literature showed only one previously reported case of pulmonary artery sling in an infant with trisomy 21. We report a case of pulmonary artery sling and complete atrioventricular canal defect in a one-month-old female with trisomy 21. Echocardiography is an important diagnostic method for pulmonary artery sling, but this anomaly may be easily overlooked in the presence of more commonly anticipated defects in this population.
KW - applications)
KW - cardiac anatomy/pathologic anatomy
KW - congenital heart disease
KW - echocardiography (all modalities
KW - tracheal stenosis
UR - http://www.scopus.com/inward/record.url?scp=84993687290&partnerID=8YFLogxK
U2 - 10.1177/2150135114526422
DO - 10.1177/2150135114526422
M3 - Article
C2 - 24958055
AN - SCOPUS:84993687290
SN - 2150-1351
VL - 5
SP - 470
EP - 472
JO - World Journal for Pediatric and Congenital Heart Surgery
JF - World Journal for Pediatric and Congenital Heart Surgery
IS - 3
ER -